Myopathic Scoliosis (मायोपैथिक स्कोलियोसिस) रीढ़ की हड्डी का abnormal lateral curvature है, जो muscle weakness या myopathy के कारण होता है।
- यह condition अक्सर congenital या neuromuscular disorders के साथ जुड़ी होती है।
- आमतौर पर progressive होती है और spine deformity, posture और mobility को प्रभावित कर सकती है।
- Severe cases में respiratory और cardiac complications भी हो सकते हैं।
Myopathic Scoliosis क्या है (What is Myopathic Scoliosis)
- Spine में lateral curvature (scoliosis)
- Associated with weak paraspinal muscles, asymmetric muscle tone
- Common in muscular dystrophies, cerebral palsy, spinal muscular atrophy
- Progression rate depends on underlying muscle disease severity
Myopathic Scoliosis कारण (Causes of Myopathic Scoliosis)
1. Muscular Dystrophies
- Duchenne Muscular Dystrophy
- Becker Muscular Dystrophy
2. Congenital Myopathies
- Nemaline myopathy
- Central core disease
3. Neuromuscular Disorders
- Spinal muscular atrophy
- Cerebral palsy
- Poliomyelitis (rare, post-infection)
4. Muscle Imbalance / Weakness
- Unequal muscle strength around spine
- Leads to progressive spinal curvature
Myopathic Scoliosis लक्षण (Symptoms of Myopathic Scoliosis)
- Visible spinal curvature (C-shaped or S-shaped)
- Uneven shoulders or hips
- Prominent rib hump on bending forward
- Difficulty in standing, walking, or sitting upright
- Back pain or fatigue
- In severe cases: shortness of breath or cardiac issues
Symptoms often worsen with growth or disease progression।
Myopathic Scoliosis कैसे पहचाने (Diagnosis of Myopathic Scoliosis)
- Physical Examination – shoulder, hip asymmetry, forward bending test
- X-ray Spine – confirms degree of curvature (Cobb angle)
- MRI / CT Scan – evaluate spinal cord and soft tissue involvement
- Muscle Function Tests – electromyography (EMG)
- Genetic Testing – if underlying muscular dystrophy suspected
Early diagnosis essential for slowing progression and planning treatment।
Myopathic Scoliosis इलाज (Treatment of Myopathic Scoliosis)
1. Non-Surgical Management
- Physiotherapy and exercises to strengthen paraspinal muscles
- Bracing / Orthotic support to slow progression
- Regular monitoring of Cobb angle
2. Surgical Management
- Spinal fusion surgery for severe curvature
- Recommended if Cobb angle >40–50° or progressive deformity
- Improves posture, mobility, and respiratory function
3. Supportive Care
- Respiratory therapy in neuromuscular disorders
- Pain management and occupational therapy
- Nutritional support for muscular dystrophy patients
Early intervention prevents severe deformity and associated complications।
रोकथाम (Prevention)
- Early diagnosis of neuromuscular disorders
- Timely physiotherapy and bracing
- Regular growth and spine monitoring in at-risk children
- Strengthening exercises to maintain core and back muscles
सावधानियाँ (Precautions)
- Avoid heavy lifting or activities that strain spine in affected patients
- Adhere to physiotherapy and brace schedules
- Monitor respiratory function in neuromuscular conditions
- Seek prompt medical care for pain, rapid curvature, or functional difficulty
FAQs (अक्सर पूछे जाने वाले प्रश्न)
Q1. Myopathic scoliosis reversible है?
नहीं, curvature permanent है, लेकिन progression physiotherapy और bracing से slow किया जा सकता है।
Q2. Surgery कब जरूरी होती है?
Severe curvature (Cobb angle >40–50°), progressive deformity या respiratory compromise में।
Q3. क्या यह दोनों sexes में होता है?
हाँ, boys और girls दोनों में हो सकता है। Risk depends on underlying muscle disease।
Q4. Physiotherapy मदद करती है?
हाँ, muscle strength maintain करने और progression slow करने में physiotherapy प्रभावी है।
निष्कर्ष (Conclusion)
Myopathic Scoliosis (मायोपैथिक स्कोलियोसिस) एक neuromuscular spine deformity है जो muscle weakness के कारण होती है।
Early detection, physiotherapy, bracing और severe cases में surgery से posture, mobility और respiratory function preserve किया जा सकता है।
अगर किसी बच्चे या वयस्क में uneven shoulders, hips या spinal curvature दिखे, तो तुरंत orthopedic / neuromuscular specialist से consultation आवश्यक है।